aphallia with urethrorectal fistula, bladder and urethral calculi

introduction: aphallia is a very rare urogenital anomaly with incidence rate of 1 in 30,000,000. it usually coexists with other anomalies such as cardiovascular anomalies which are incompatible with normal life, and therefore infants are delivered stillbirth or live for a very short period of time. methods: we present an 18 months old boy with aphallia associated with congenital urethrorectal fistula, bladder and urethral stones. all stones were removed endourologically, recto-urethral fistula was repaired and perincal urethrostomy was performed. results: the stones were composed of calcium phosphate colonized by klebiella pneumonia and proteus mirabilis. urethrorectal fistula repairment was confirmed by cystography. patient was discharged without a urinary catheter. conclusion: in developed countries, management of such patients is to raise them as females. however, we must consider socio-cultural conditions, parents preference and patients tendency in management of aphallia.